Pyruvate Kinase (PKLR) Mouse Monoclonal Antibody [Clone ID: LBI1A5]-抗体-抗体-生物在线
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Pyruvate Kinase (PKLR) Mouse Monoclonal Antibody [Clone ID: LBI1A5]

Pyruvate Kinase (PKLR) Mouse Monoclonal Antibody [Clone ID: LBI1A5]

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产品名称: Pyruvate Kinase (PKLR) Mouse Monoclonal Antibody [Clone ID: LBI1A5]

英文名称: Pyruvate Kinase (PKLR) Mouse Monoclonal Antibody [Clone ID: LBI1A5]

产品编号: AMM10006V

产品价格: null

产品产地: 美国

品牌商标: Leading Biology

更新时间: null

使用范围: WB 1:500

安诺伦(北京)生物科技有限公司
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别名:PK1; PKL; PKR; PKRL; RPK

产品概述:PKLR mouse monoclonal antibody, clone LBI1A5

总结:The protein encoded by this gene is a pyruvate kinase that catalyzes the transphosphorylation of phohsphoenolpyruvate into pyruvate and ATP, which is the rate-limiting step of glycolysis. Defects in this enzyme, due to gene mutations or genetic variations, are the common cause of chronic hereditary nonspherocytic hemolytic anemia (CNSHA or HNSHA). Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq]